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Yayın Goldenhar syndrome with situs inversus totalis(Munksgaard, 1998) Görgü, Metin; Aslan, Gürcan; Erdoğan, Bülent; Karaca, C.; Aköz, TayfunGoldenhar syndrome (oculo-auriculovertebral spectrum) is a common disorder with a birth prevalence of about one case per 5600 births. The syndrome has been rKviewed extensively elsewhere 1'2. Hundreds of cases have been reported. We present a case of Goldenhar syndrome with total situs inversus. An affected 15-month-old female is shown in Fig. 1. The father had been operated on for ear anomalies 20 years earlier. Radiographs (Fig. 2) demonstrated vertebral anomalies, scoliosis, and dextrocardia. Ultrasonagraphic examination (Fig. 2) showed a left-sided liver and a right-sided spleen. To our knowledge, situs inversus totalis has not previously been reported with Goldenhar syndrome.