Goldenhar syndrome with situs inversus totalis

Küçük Resim Yok

Tarih

1998

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Munksgaard

Erişim Hakkı

CC0 1.0 Universal
info:eu-repo/semantics/openAccess

Araştırma projeleri

Organizasyon Birimleri

Dergi sayısı

Özet

Goldenhar syndrome (oculo-auriculovertebral spectrum) is a common disorder with a birth prevalence of about one case per 5600 births. The syndrome has been rKviewed extensively elsewhere 1'2. Hundreds of cases have been reported. We present a case of Goldenhar syndrome with total situs inversus. An affected 15-month-old female is shown in Fig. 1. The father had been operated on for ear anomalies 20 years earlier. Radiographs (Fig. 2) demonstrated vertebral anomalies, scoliosis, and dextrocardia. Ultrasonagraphic examination (Fig. 2) showed a left-sided liver and a right-sided spleen. To our knowledge, situs inversus totalis has not previously been reported with Goldenhar syndrome.

Açıklama

Anahtar Kelimeler

Kaynak

WoS Q Değeri

Scopus Q Değeri

Q1

Cilt

27

Sayı

5

Künye

Görgü, M., Aslan, G., Erdoğan, B., Karaca, C. ve Aköz, T. (1998). Goldenhar syndrome with situs inversus totalis. International Journal of Oral & Maxillofacial Surgery. 27(5), s. 404.